Philippe Camus, M.D.

Dijon, France

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X.o

X - Systemic/Distant conditions, syndromes and reactions

Vascultis (pulmonary, extrathoracic or systemic)-ANCA status unknown or negative)

Last update 23/07/2021

Can be granulomatous in nature (PMID 34237323). Older literature does not mention ANCA status (See under Xs). Can involve the lung, deep-seated organs (liver, kidney), viscerae, brain, extremities and/or skin or be diffuse (polyangiitis) clinically mimicking granulomatosis with polyangiitis (formerly known as Wegener's). See also under IIId and VId

Causative drugs

35

Frequency - Incidence

Incidence of respiratory adverse event(s) due to the specific drug as assessed by number of reported/published cases in the literature. Red digits in stars indicate: 0 = Very rare, questionable signal · 1 = < 10 cases · 2 = 10-50 cases · 3 = 50–100 cases · 4 = 100-200 cases · 5 = >200 cases

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