XLIX - Systemic/Distant conditions, syndromes and reactions
Vascultis (pulmonary, extrathoracic or systemic)-ANCA status unknown or negative)
Last update 23/07/2021
Can be granulomatous in nature (PMID 34237323). Older literature does not mention ANCA status (See under Xs). Can involve the lung, deep-seated organs (liver, kidney), viscerae, brain, extremities and/or skin or be diffuse (polyangiitis) clinically mimicking granulomatosis with polyangiitis (formerly known as Wegener's). See also under IIId and VId