Philippe Camus, M.D.

Dijon, France

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XLVI.d

XLVI - Pulmonary vasculopathy

Pulmonary vasculitis or capillaritis

Last update 17/06/2026

Including granulomatosis with polyangiitis. With or without ANCA or DAH present. Capillaritis is sometimes documented on pathology. In cases due to PTU or cocaine/levamisole, very high titres of multispecific ANCA can be present. See also under III and XII

Causative drugs

24

Frequency - Incidence

Incidence of respiratory adverse event(s) due to the specific drug as assessed by number of reported/published cases in the literature. Red digits in stars indicate: 0 = Very rare, questionable signal · 1 = < 10 cases · 2 = 10-50 cases · 3 = 50–100 cases · 4 = 100-200 cases · 5 = >200 cases

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